This paper presents the case of a 5-year-old child with severe haemophilia A treated for epidural bleeding into the CNS resulting from spine trauma. Every case of CNS trauma in children with haemophilia entails a high threat to life and limb, and as a priority requires factor VIII supplementation and further urgent diagnostics. Treating a child with CNS bleeding in the course of haemophilia requires the cooperation of a team of specialists, including a haematologist, radiologist, neurosurgeon, orthopedist and rehabilitation specialist. The treatment strategy in itself and selection of a conservative or surgical treatment method require an in-depth analysis. Supplementation treatment should be initiated immediately following the diagnosis of a head or spinal column injury, or after the onset of signs and symptoms indicating CNS bleeding.